Touraine Polykeratosis

Touraine polykeratosis: main characteristics and treatment

Touraine polykeratosis, also known as Turaine's disease, is a rare genetic disorder that occurs in the form of hereditary ichthyosis. Ichthyoses are a group of disorders characterized by dry and flaky skin caused by increased formation and delayed exfoliation of horny scales.

The name Touraine's polykeratosis comes from the French dermatologist Albert Tourain, who first described the disease in 1907. Touraine polykeratosis is a hereditary disease and can run in families.

The main clinical manifestations of Touraine polykeratosis are dry skin, flaking, as well as rough and hyperkeratotic (thick) skin on various parts of the body. These skin changes may be localized or distributed throughout the body. The extremities are most commonly affected, especially the elbows and knees. In some cases, Touraine's polykeratosis may be accompanied by other symptoms, such as curled nails or hair loss.

Treatment for Touraine polykeratosis is aimed at softening and moisturizing the skin, as well as controlling the growth and exfoliation of horny scales. The main treatment approach involves the use of emollients and gentle cleansers to care for the skin. Regular use of urea, lactic acid or salicylic acid can help exfoliate horny scales and soften the skin.

Additionally, systemic treatment may be offered in severe cases of the disease. Retinoids, such as isotretinoin or akitretin, can be used to improve skin condition and reduce the thickness of the horny scales. However, it should be noted that each case of Touraine polykeratosis is unique, and treatment must be individualized for the individual patient.

At the same time, it is important to consult a dermatologist to obtain an accurate diagnosis and develop a treatment plan. A dermatologist will be able to assess the condition of the skin, determine the severity of the disease and provide recommendations for skin care.

Although Touraine polykeratosis is a chronic condition, with proper skin care and treatment, most patients will be able to reduce symptoms and improve their quality of life.