Miescher-Storka syndrome

**Mischer-Stohrock syndrome** is a rare hereditary autosomal dominant multisystem and multifocal degenerative process with autoimmune components, directed against its own peripheral and central components of the integument. The disease is congenital in nature and manifests itself in childhood or adolescence with signs of damage to the nervous system, skin, cardiovascular, urinary and reproductive systems. Dermatologists, geneticists, neurologists, cardiologists and nephrologists are involved in the diagnosis and treatment of the disease. Patients with Miescher syndrome -