Papillon-Leage-Psoma Syndrome

Papillon Leage Psoma Syndrome (PAPPS) is a rare genetic disorder that causes abnormal development of teeth and gums. This disease was first described by French dentist Eugene Papillon in the 20th century.

The main features of this syndrome are dental abnormalities, including missing teeth, their irregular position and shape. There may also be gum abnormalities, such as thinning or thickening of the gums.

Treatment for PAPPS may include surgical correction of abnormal teeth and gums, as well as the use of special dentures to cover the defects. However, since it is a genetic disease, it is not completely curable.

Although PAPPS is a rare disease, it can cause serious health problems, including problems with eating, speaking, breathing and even life. Therefore, if you suspect PAPPS, you should see your dentist for diagnosis and treatment.



Papillon-Leage-Psama syndrome is a group of hereditary diseases of the dental system, in which, due to genetic mutations, abrasion of enamel, malocclusion and jaw bones, and inflammatory processes that lead to tooth destruction develop. With this disease, destruction of the hard tissues of the tooth occurs, i.e. Foci of enamel demineralization and the appearance of cracks are observed. The disease can lead to deformation and curvature of the jaw, which can significantly impair the patient's quality of life. The main symptoms of Papillon Leage Syndrome are pain in the jaw area, tooth sensitivity to hot and cold foods, bleeding gums, bad breath and discoloration of enamel. If the disease is not treated, the teeth may become damaged and the gums may become inflamed.

Papillon-liages-psama syndrome was first described by French dentist Paul Lucien Papillon in the 70s of the 20th century. Subsequently, it was named after the French dentists Jacques Psaume and Mathilde Leage, who studied this disease and found a way to treat it. We treat this disease by combining various techniques, including professional oral hygiene, ultrasonic cleaning, hardware treatment, root canal filling, prosthetics or implant installation. Treatment of Papillon-Leage-Dog Syndrome goes a long way with its patients. Treatment in the early stages of the disease, when teeth and gums are healthy, can help keep teeth looking healthy for a long time. However, if the disease progresses rapidly, the prognosis is less favorable and possibly