Chiari Disease

Chiari Disease: Understanding and Symptoms

Chiari disease, also known as primary hepatic vein thrombosis, chiari disease or endophlebitis occlusives of the hepatic veins, is a medical condition that was described by the Austrian pathologist Chiari in 1851. This rare pathology is characterized by abnormal placement of the brain stem and cerebrum, which can lead to a variety of neurological symptoms.

The main symptom of Chiari disease is the displacement of the lower part of the brain, known as the cerebrum, down through an opening in the skull called the foramen magnum. This displacement results in compression of the brain stem and spinal cord, which can lead to various neurological manifestations.

Symptoms of Chiari disease can be varied and depend on the degree of shift in brain structures and compression of nerve tissue. Some patients may experience headaches, especially in the back of the head, which may worsen with coughing or straining. Dizziness, nausea and vomiting may also be present.

Patients with Chiari disease may also experience sleep problems, including insomnia and sleepiness during the day. There may be problems with coordination of movements, unsteadiness when walking and instability. Some patients have problems with motor skills and sensation in the arms and legs, as well as muscle weakness.

The diagnosis of Chiari disease is usually based on clinical symptoms and the results of additional tests. Magnetic resonance imaging (MRI) of the head and cervical spine can help visualize the displacement of brain structures and determine the degree of compression.

Treatment for Chiari disease varies and depends on the severity of symptoms and progression of the disease. In some cases, surgery may be necessary to improve the circulation of cerebrospinal fluid and release compressed structures. However, the decision about the need for surgery is made individually for each patient.

Overall, Chiari disease is a rare and complex condition that requires close medical monitoring and management. Timely diagnosis and adequate treatment can help improve the patient's quality of life and reduce the risk of complications.

Chiari disease

*Chiari disease* is a neurological disease characterized by the displacement of the cerebellar tonsils down into the spinal canal of the spine. It usually occurs in adults, but can also occur in childhood.

Causes

The main reasons for the development of the disease have not yet been precisely established. The pathology is assumed to be congenital. Possible causes are non-fusion of the cerebellar and spinal cord of the fetus, disruption of the relationship between them or problems with the muscles that support the head, problems in the formation of the spinal column. The influence of negative environmental factors and heredity is also assumed. In some cases, chiari disease develops due to acquired injuries to the spinal cord or brain. Often the occurrence of chiari disease is accompanied by tumors. Symptoms may appear after injuries or infectious diseases of the nervous system. The causes of the development of the disease also include epidemic cerebrospinal meningitis, acute or chronic brain disorders