Chronic familial polyserositis: understanding and treatment
Introduction:
Chronic familial polyserositis (polyserositis chronica familiaris) is a rare hereditary disease characterized by inflammation of the mucous membranes of various body cavities. This condition can have a significant impact on patients' quality of life and requires a comprehensive approach to diagnosis and treatment. In this article we will look at the main aspects of chronic familial polyserositis, including its symptoms, causes and modern treatment methods.
Symptoms of chronic familial polyserositis:
Patients suffering from chronic familial polyserositis experience chronic inflammation of the mucous membranes of various organs. The main symptoms associated with this disease include:
- Pain in various areas of the body such as the chest, abdomen and joints.
- Difficulty breathing and chest pain caused by inflammation of the pleura and pericardium.
- Fluid in organ cavities such as the pleural, pericardial and abdominal cavities, which can lead to swelling and discomfort.
- Feeling tired, general weakness and loss of appetite.
Causes of chronic familial polyserositis:
The causes of chronic familial polyserositis are not fully understood. However, research points to a genetic factor playing a role in the occurrence of this disease. The disease can be inherited from one generation to the next, although the exact mechanism of inheritance is not yet clear.
Modern methods of treatment:
Treatment of chronic familial polyserositis is based on a symptomatic approach aimed at relieving symptoms and preventing complications. Here are some of the modern treatments:
- Nonsteroidal anti-inflammatory drugs (NSAIDs): These are used to reduce inflammation and relieve pain. Examples of NSAIDs include ibuprofen and diclofenac.
- Glucocorticosteroids: These drugs may be used to reduce inflammation and suppress the immune response. They can be given by injection or taken orally.
- Treatment of fluid retention: If chronic familial polyserositis causes swelling, diuretics may be required to remove excess fluid from the body.
- Surgery: In rare cases, when chronic familial polyserositis leads to serious complications, surgery may be required. For example, drainage of the pleural cavity may be performed to remove accumulated fluid.
Conclusion:
Chronic familial polyserositis is a rare genetic disease characterized by chronic inflammation of the mucous membranes of various body cavities. The symptoms of this disease can significantly affect the quality of life of patients. Although the causes of chronic familial polyserositis are not fully understood, modern treatment methods are aimed at relieving symptoms and preventing complications. It is important to conduct further research to better understand the mechanisms of development of this disease and develop more effective treatments.
Polyserositis - what kind of disease?
**_Family polyserositis (chronic)_** _- _characterized by a recurrent course with exacerbations 2 times a year or more - progressive extrapulmonary symptoms from many organs and systems, leading to decreased performance, loss of previous functions