Batten S Disease

Batten disease

Batten disease is a recessive inherited disorder that results in the accumulation of fatty substances in nerve cells. This is a rare disease that usually appears in early childhood but can develop at any time in life.

Symptoms of Batten disease usually include progressive dementia



Ever since Batten Disease became known, there has been confusion in medical circles. The disease manifested itself with symptoms that seemed to resemble other neurological diseases, such as Alzheimer's disease. However, many scientists did not see a clear connection between these two diseases. Although the accumulation of pathogenic fats was also observed in Alzheimer's disease, lipids accumulated in neurons differently than in Batten, and their effects and consequences were completely different. Research is still underway and data on the new disease are being discussed. But what is certain is that we need to have a greater understanding of what factors determine Batten disease. If medicine can understand why the immune system stops functioning, then perhaps we will find a way to help it. In addition to research aimed at understanding the disease itself, we also need to think about the possible consequences of the stem cell transplant experiment itself. Did the transplant really give positive results? Or could it harm other people? If researchers can confirm its safety, it may be safer to target these methods to other rare diseases, such as Harry Hawkings disease and Warther's disease.