Dandy-Walker Disease

Dandy-Walker disease

Dandy-Walker disease is a disease described by American neurosurgeons Walter Edward Dandy (1886-1946) and Arthur Earl Walker (born 1907).

It is characterized by impaired circulation of cerebrospinal fluid, which leads to hydrocephalus. The cause is an abnormal development of the cerebellum with partial or complete obstruction of the foramina connecting the fourth ventricle of the brain with the subarachnoid space. Clinically manifested by an increase in the size of the skull, bulging of a large fontanel, headache, vomiting, blurred vision and other symptoms of increased intracranial pressure.

Diagnosis is based on neuroimaging (CT, MRI), which allows to identify signs of cerebral hydrocele. Treatment is surgical, aimed at restoring the outflow of cerebrospinal fluid. The prognosis with timely treatment is favorable.