Corpus striatum syndrome

Striatal syndrome

Striatal (spinal) syndrome (Millard-Grandy syndrome) is a rare hereditary disease characterized by progressive lag in psychomotor development, dystonia, extrapyramidal dyskinesia syndrome, epileptic seizures of various forms, pseudobulbar disorders and other changes. The classic variant of the syndrome is characterized by motor phenotypes described as “choreoathetosis,” “thoracic scoliosis,” and “striatal dystonia.” The syndrome is much more widespread than the frequency of described cases indicates, precise data on