Tentorial Syndrome Description of the syndrome Tentorial Syndrome - Not included in the international classifier of diseases. Belongs to the category of retrograde dysphagia. The disease belongs to the category of neurological diseases, namely neurological disorders of brain function
Tentorial process syndrome or Sundblom syndrome (Latin “tentorium” - “tentorium” + Latin “syndromus”) is not a separate disease or even a disorder, but a so-called familial syndrome. In simple words, this is a group of diseases (sometimes multisystem) that are accompanied by pain in the skull, neck, shoulder or other part of the body.
The syndrome is caused by damage to the tentorium - the lowest part of the brain, which protects the brain with the help of a special muzzle. Inflammation or other damage within this part of the brain provokes uncontrollable attacks of pain or other disorders, which in some cases may not appear until adulthood or may not occur at all even in old age.
The term “syndrome” translated from ancient Greek means “connection”, “connection”. In simpler terms, we are talking about several interrelated pathological conditions of a particular organ or system of the body. The main cause of Sundblom syndrome is genetic factors. The exact hereditary nature of the syndrome is still a matter of debate. There are two known genotype variants in which the risk of developing the syndrome increases significantly: deletion of a section of chromosome 5q13.3 and deletion of the short arm of chromosome X. In addition, as genetic data accumulate, it is increasingly possible to trace the connection between Sandlobm syndrome and hereditary parathyroid adenoma (Olbre syndrome