Lymphangioblastoma

Lymphangioblastoma (LB) is a rare tumor that originates from the lymphatic vessels and is a malignant neoplasm that can spread to nearby tissues and organs. In this article we will look at what LB is, its symptoms, causes and treatment.

*Lymphangioma* is a formation consisting of benign lymphangial vessels (lymphatic channels), which are usually located on the surface of the skin or inside the body. It can be either congenital or acquired as a result of injury or radiation. In addition, LB can be asymptomatic and remain in the human body for a long time without causing any problems. However, in some cases it can lead to serious illnesses such as pulmonary edema or lymphatic clot.

Lymphangiomablastoma is a rare tumor of the lymph and lymph nodes within the body. In the vast majority of cases, this tumor, when localized on the skin and sensory organs, is located on the sternum or neck. Only in 20-40% of cases are neoplasms found in other areas of the body. When large in size, these tumors can compress organs in the thoraco-abdominal region. The risk of developing lymphangioblastoma is higher in males. It is the most common soft tissue tumor of the maxillofacial region in children after Ewing's sarcoma (from 3.5 to 7.5 per 1,000