Fibromatosis Juvenile Aponeurotic

Fibromatous aponeurosis is a type of extracellular diffuse disease called muscle fibromatosis. If you look at the English term, you will find the word “fibrilla” in it, which means “strong, dense fibrous tissue.” Accordingly, this suggests that in this case the fibromuscular structure is affected, and this is typical not only for the muscles and external tissues of the body, but also for the skin.

It is worth noting that according to the International Classification of Diseases, Tenth Revision, fibromatosis of the muscular type is not assigned a code in the classification system. In ICD-10 it corresponds to one of the rare endocrine diseases - diffuse mastopathy syndrome, as well as an undistributed form of fibrodysplasia. Both options do not present any particular diagnostic difficulty. At

Fibromatoses are benign connective tissue diseases that are characterized by the formation of keloid scars and tough, wood-like tissue lesions. In rare cases, the etiology of the disease is unclear, but in most cases, fibromatosis develops in people with weak immune systems and in people exposed to ultraviolet radiation (for example, on the beach, in a tanning bed, or while wearing sunglasses).

Fibromatosis Juvenile Aponeurotica (JA) is a disorder of the skin's connective tissue due to gene mutation that occurs in people between the ages of ten and thirty. This tumor is a small lump in the lower abdomen that can cause discomfort. FUA is a pathological condition of connective tissue and belongs to the group of non-malignant tumor processes.

The occurrence of juvenile aponeurotic fibromatosis is associated with hereditary factors: defective genes of the 1st chromosome (