Nephrosis Pigment

Nephrosis pigmentosa is a rare disease that affects the kidneys and can lead to death if left untreated. This disease is diagnosed in people of all ages, but most often occurs in children aged 8 to 12 years. Nephrosis differs from ordinary allergies or bronchial asthma in that it is not associated with hypersensitivity of the immune system. The cause is unknown. Symptoms include recurrent swelling of the face, sometimes progressing to swelling of the throat, lungs and abdomen. There may be facial flushing, bright erythema on the cheeks and neck, and there may be a mottled or reddish-brown tint to the skin. Severe itching and the formation of dry crusts on the skin with a pronounced port wine color are typical. Nephrotic pneumonia most often affects the lower respiratory tract and quickly spreads throughout the respiratory system. There are also known cases of damage to the urinary tract. A urine test may show albuminuria, while a blood test may show elevated blood cholesterol levels. In the acute stage of the disease, mortality can reach 25%, but with adequate treatment, patients recover well. Treatment includes dietary changes, medications such as steroids and immunosuppressants.