Roussy-Lhermitte-Schelvena Syndrome

Roussy-Lhermitte-Schelven syndrome (RUSSI-LHÉRITTE-SCHELVEN SYNDROME), also known as MOUSE - Mediated Unilateral Sensorimotor Loss with Extrapetrosomal Neuropathy, is a rare but potentially serious neurological disorder. It was first described in the 1970s by three French doctors, Guillaume Roussy, Jean-Jacques Lhermitte and Louis-Albert Chelvin. This syndrome is characterized by isolated loss of movement and sensation on one side of the body, usually occurring at or shortly before birth. Overactivity of brainstem motor neurons leads to loss of motor control, causing falls and other movement disorders on the affected side. The syndrome can be caused by a variety of factors, including heredity, infections, trauma, medications, and other diseases. Treatment of the syndrome requires an individual approach and may include special motor exercises, drug therapy and physical therapy. Overall, Roussy–Lhermitte–Shenwen syndrome is an important diagnostic and research discovery in neurology that sheds light on many aspects of human psychology and physiology.

Roussy-Lhermitte-Schelven syndrome, or Friedreich's disease, is a hereditary disease of various muscle groups, mainly cardiovascular, respiratory and masticatory. It is one of the forms of disorders of fatty acid metabolism in humans. This disease has several names - Stelven syndrome