Netherton Syndrome

Netherton syndrome is a rare hereditary disease characterized by severe skin and immune disorders. The syndrome was discovered and first described in 1939 by Canadian dermatologist E. W. Netherton.

Terton syndrome occurs in children and adolescents aged 6 months to 18 years. It affects the skin and leads to multiple skin rashes that include dermatitis, eczema, macules and lichenification. Patients also experience episodes of fever caused by infections or inflammatory reactions.

The main manifestation of non-Terton syndrome is eczema, which can lead to severe itching and pain. The most common types of eczema associated with the syndrome are called atopic and striatal. In addition, in non-Terton syndrome, macular and linear patterns called Langerhan's lines may occur. These linear features on the skin may be keratinized or tender. They are often found on the neck, ankles and wrists.

In addition to skin manifestations, Terton syndrome is characterized by a disorder of the immune system. This means that people with this syndrome have an increased risk of developing infections, including infections of the respiratory tract, ear, nose and throat, and eyes. They may also be more sensitive to allergic reactions.

Diagnosis of non-Terton syndrome is based on the detection of characteristic symptoms and confirmation of the connection with genetic tests. Treatment for this condition typically involves a variety of treatments, such as antihistamines, immunosuppressants, moisturizers, and dietary changes.

Overall, Netherton syndrome is a serious condition that has a significant impact on health and quality of life.

Netherton syndrome

Netherton syndrome is an inherited inflammatory skin disease that causes dryness, flaking, redness and scaling. The syndrome can develop at any age, but most often appears after 40 years. The disease is accompanied by long-term treatment. It