Dysplasia Ectodermal Multiple

Epithelial dysplasia is a type of cancer pathology. Only keratinization of any tissue can be called oncology. Oncology is a group of malignant neoplasms and precancerous diseases of epithelial tissues, which is under the control of the International Agency for Research on Cancer, the Inter-American Cancer Bank and the Royal College of Scrubber and Trust, but each country has its own standards for diagnosis. Therefore, an unqualified attitude towards this disease can not only aggravate the patient’s condition, but also lead to his death. Dysplasia appears immediately and quite often causes

Dysplasia of the exodermal epithelium (or dysplasia of the ecdermal islands, multiple or random transformation of root-like protrusions into exodermal islands) belongs to the group of dystrophic processes in the differentiating plasticity of somatic cells, as well as one of the rare hereditary diseases with an autosomal recessive type of inheritance.

Normally, the ectoderm layer forms the integumentary tissue: skin, its derivatives: hair, nails, bone tissue. Disturbances in the embryonic development of the exodermal zone of the skin in EM (multiple ectoderm dysplasia) are associated with the appearance, instead of the normal exodermal epidermis, of heterogeneous proliferative formations called ectodermal islands, consisting of a complex of features characteristic of the skin.

Congenital ectodermatodysplasia multiforme (ECD) type A

Type A is most often associated with a male predisposition (juvenile eczematous eryselotomy). In children of this type of ECD, pathological manifestations are more diverse and are more often found on the skin and mucous membranes of a multiple nature:

* Very often there is damage to the mucous membranes - fungal, candidal, toxic, independent; often the phenomenon of erythema in the mouth, pharynx, external auditory canals. * As the child grows, acne and or acne-like elements appear, jaundice, and hyperpigmentation of the extensors. In boys, a common clinical form may be a cyst of the spermatic cord * Sometimes lesions like eczema, hyperemia of the skin, follicular hyperkeratosis, ochronorosis, colloid scars appear on the skin * Infrequently, but associated with type a fever of unknown origin, possible development of cirrhosis of the liver and cataracts.