Hirschsprung's disease is a congenital malformation of the rectum, and sometimes the distal colon, resulting from denervation of all elements of the intestinal wall and blood vessels. In this case, the passage of intestinal contents through the affected areas is disrupted, which leads to its accumulation in the overlying part of the colon and subsequent distension.
Symptoms of the disease often appear in the first week of a child's life. These include abdominal pain, bloating and severe or complete constipation.
The diagnosis is made on the basis of an X-ray examination and a biopsy of the intestinal wall, which reveals the absence of nerve cells in the affected area.
Treatment involves surgically removing the affected part of the colon and creating an anastomosis between the remaining (normal) part of the colon and the rectum.
See also: Megacolon.
Hirsprung S disease is a congenital defect characterized by impaired passage of intestinal contents through the intestine due to the complete absence of nerve cells. This defect is often found in children and requires immediate intervention, as it causes severe pain, bloating and constipation, and if left untreated can be fatal. A birth defect develops due to a disruption of nerve conduction in the rectal area. This manifests itself in the form of a congenital expansion of its walls and the absence of nerve cells responsible for the contraction of muscle fibers. There is a high probability of developing intestinal obstruction,
Hirschsprung's disease, also known as Hirschsprung's disease or Hirschsprung's syndrome, is a rare congenital disorder associated with abnormal development of nerves in the intestine. This anomaly is characterized by the absence of nerve endings in an extended segment of the intestine, called aganglionosis, and is caused by partial loss or blockage of nerve cells, usually during the embryonic stage of development.
Heirsprog's disease can present with a variety of symptoms, including constipation, bloating and pain. In some people, Hirsprög's disease does not appear until adulthood due to delays in intestinal development. In other cases, symptoms may become apparent in newborns.
Infants with Hersprug's disease usually develop symptoms within the first week of life. Sometimes the first sign may be loose stools, followed by constipation soon after birth. By two weeks of age, babies develop growth retardation and poor weight gain. Over time, pain appears in