Charcot syndrome is a chronic progressive disease, a type of hereditary sensorineural deafness and anosmia (loss of smell function).
The origin of the name of the syndrome is associated with the name of the French doctor of Italian origin, Jean-Martin Charcot. He was the first to describe the pathology in 1886. Several forms of the disease were identified, but the criteria by which they could be distinguished from one another were not formulated at that time. Work on this continued until the beginning of the 20th century. But during this time, several revolutions took place in medicine, putting forward new requirements. Charcot ceased to be the only one and taken for granted, and more and more of his research began to be published in specialized journals by scientists - otolaryngologists and other clinicians. Only then was it possible to finally recognize several forms of the disease and determine the criteria for its differentiation.
The main symptom of the disease is a sharp decrease in the level of hearing and sense of smell. In this case, deafness in patients may be periodic (for a short time the ears begin to hear better