Darier-Ferrand Dermatofibrosarcoma

Darier-Ferrand dermatofibrosarcoma

Darier-Ferrand dermatofibrosarcoma is a rare malignant skin tumor related to soft tissue sarcomas.

This is a slowly growing tumor that primarily affects the skin and subcutaneous tissue. Most often occurs in adults aged 20-50 years. It most often affects the lower extremities, less often the head, neck and torso.

Clinically manifests itself as a dense, painless nodule or nodule that may ulcerate. The tumor slowly increases in size, forming plaques and nodes of various shapes.

Diagnosis is based on histological examination. Surgical treatment involves excision of the tumor within healthy tissue. The prognosis is favorable with early diagnosis and adequate treatment. Relapses are possible, so dynamic monitoring is necessary.

Darier-Ferrand Derimatofibrosarcoma. (J. Darier,1858 - 167, Franclans Dermaltonique) Franc.). M. Ferrand,1879 - 56, Franc.)

(French dermatologist - Jacques-Marie Caillot, January 22, 1756 - September 2, 1833)

The first mention and origin of the name of the disease is still quite unclear.

> He emphasizes that the name is given in honor of Jacques-François Deroyan, representing the department of surgery of the Saint-Louis Hospital (Paris), a famous surgeon and an excellent neurologist (Deroyan was his contemporary). Deroyan seems to have pioneered and pioneered the clinical classification of benign skin lesions. He has priority in the study of warts, acne (neonatal acne) and other skin diseases (Kaya's contribution). A. Philaber describes a family of patients suffering from benign skin neoplasms in connection with juvenile skin disease of Ferrans, after whom dermatofibrotic xaxopoii (dermatofibratosis) and Ferrache's disease are named based on his work.

Darier Ferrand and Dermatofibrosarcoma (also known as a sarcoid form of benign dermal tumor) are unique diseases encountered in dermatology. This pathology is characterized by the appearance on the skin of benign tumors consisting of connective tissue that are prone to malignancy (degeneration into a malignant neoplasm).

The French gave the name to this pathology because of its unusual properties, in which its symptoms surprisingly resemble