Dystrophy Pigmentary Hemoglobinogenic

Pigmentary hemoglobin dystrophy

Dystrophic pigmentary diffuse aleukia (DPDA) is a rare, little-studied disease of the bone marrow, characterized by a progressive deficiency of erythropoietin, red blood cells and hemoglobin, as well as hypercellularity of the bone marrow.

Pigmentary hemolytic anemia (PHA) is a hereditary disease characterized by hemolysis of erythrocytes caused by the functional inferiority of one of the globin chains or two subunits of the chain, as well as their heteroduplexing disorder. Clinically, PHA manifests itself as apla