Erythrokeratoderma Progressive Symmetrical

Erythrokeratoderma Progressive Symmetrical: symptoms, diagnosis and treatment

Erythrokeratoderma progressive symmetric (ESPS) is a rare genetic skin disease that manifests itself as a disruption of melanin pigment cells and keratinocytes. It is characterized by symmetrical skin lesions that begin on the extremities and gradually spread to the trunk.

Symptoms

The main symptoms of ESPS are dryness, flaking and redness of the skin. The skin becomes rough and rough, red spots appear, which eventually merge into one large spot. In addition, the formation of cracks and ulcers on the skin is possible. The disease can lead to dysfunction of the hands and feet, as well as cosmetic defects.

Diagnostics

Diagnosis of ESPS is based on clinical symptoms and skin biopsy results. It is important to carry out differential diagnosis with other diseases such as psoriasis, eczema and dermatitis.

Treatment

Although ESPS does not have a complete cure, there are methods that help improve the quality of life of patients. It is important to monitor the condition of the skin and regularly moisturize, as well as use emollient creams and ointments. In some cases, phototherapy may be prescribed to help reduce redness of the skin. Immunomodulatory drugs such as topical corticosteroids may also be used.

In conclusion, Erythrokeratoderma Progressiva Symmetric is a rare but serious skin disorder that can lead to impaired limb function and negatively impact the patient's quality of life. It is important to consult a dermatologist in a timely manner for diagnosis and effective treatment.

Erythrokeratosis is one of the forms of generalized hyperkeratoses, manifested by symmetrical red foci of various shapes and sizes, covered with callous horny layers. It occurs as a result of dystrophic changes in the epidermis and disorders of reparative processes along the hypogranular line, metachronous in relation to lesions in the skin. The flat form of erythrokeratosis can be an independent nosological form. The disease occurs predominantly in women. E. should be distinguished from lichen planus and multiple actinic keratosis.