Dysplasia Fibrous Familial

**Fibrous dysplasia familial** (dysplasiafibrosafamilialis) is a hereditary lesion of the connective tissue of the bronchi and aortic vessels with a clinical picture of recurrent attacks of pulmonary artery stenosis. This group of diseases includes the same von Willebrand syndrome - a disease of the circulatory system, which often causes additional symptoms in the patient, such as shortness of breath and the inability to remain in an upright position for a long time. Children with this condition develop serious defects in the functioning of the cardiovascular system, which can cause death for the child.