Epidermolysis Bullous Congenital Hyperplastic

Congenital epidermolysis bullosa is a rare hereditary disease characterized by damage to the skin as a result of multiple blisters that form on the skin of the limbs and torso. It is one of the ten most common hereditary human diseases. Treatment of the disease is difficult and requires the use of special moisturizing preparations, proper skin care and treatment of infectious complications.

Congenital epidermolysis has three forms of the disease - benign, malignant, borderline or bullous Erber's dermodysplasia. The type of skin manifestations also depends on the degree of changes in the structure of the skin. The disease is accompanied by increased sensitivity of the skin to physical and chemical influences. Is there such a disease in the world? – yes, because it is congenital, that is, from birth there will be such sensitivity of the skin. A person is born with altered skin, which, when severely irritated, begins to react precisely to the chemical odors of cosmetics and to the pressure that is exerted on it. In the very first years, and some even in childhood, they cannot take a shower, bathe, or do other ordinary things, because these manipulations cause pain.

Congenital hyperplastic epidermolysis bullosa is a rare hereditary disease of the skin and mucous membranes that develops due to a defect in the membrane between the epithelium and the underlying layers of the skin or in the connective tissue layer of the skin. This defect causes the skin to become too thin and more prone to blistering.

Different areas of tissue can be affected, and most often