Lymphangioendothelial sarcoma

Sarcoma lymphangioendothelioma (Lymphatic endothelial-histiocytic sarcomas) - the tumor has two components - lymphoid elements (lymphoblasts) and endothelial cells. The tumor often contains T lymphocytes. Occurs in young people. It is believed that this type of sarcoma is formed from hybrid cells of lymphatic vessels and endothelial tissue. Typically located in the neck, head and shoulders, legs and arms. Symptoms may include swollen lymph nodes, fever, and swelling of the lungs and nearby tissues.

The reasons for the development of lymphosracomatosis are hereditary factors - one of the rarest genetic diseases: Li-Fraumeni syndrome and childhood lymphangiosarcoma, caused by abnormalities of chromosome 6p12.

Treatment usually consists of surgery and radiation therapy.

Lymphangioedeal sarcoma (Sarcoma of the endothelium of blood vessels and lymphatic vessels)

Lymphangioedothelial sarcomas are one of the rarest and most severe malignant tumors. They develop from hematopoietic (blood-forming) precursor cells. According to one of the sources, it got its name “lymphosarcoma”, since developing cells of the type are considered one of the components of the lymphatic