Weber-Cockayne Syndrome

Weber and Cockayne syndromes

Weber and Cockayne syndromes (Weber stroke and Locke syndrome) are bilateral spinal cord palsies that can lead to paralysis of the body or limbs. They arise from tears in the fibers of the corticospinal tract at the base of the brain. In this case, the pyramidal tracts are damaged. This process is often the result of a head injury or severe infection. It is important to note that these syndromes can have varying degrees of severity and lead to different consequences.

Symptoms

Symptoms of Weber and Cockayne syndromes may include: - loss of sensation in the limbs, - weakness or inability to move in the affected limbs, - difficulty walking and loss of coordination.

In more severe cases, complete paralysis of the trunk or even respiratory failure may occur. In some cases, coma may be associated with this syndrome.

Article "Weber-Cockayne syndrome"

The problem of the syndrome is not only medical, but also social and mental. Weber–Cockayne disease (WCC) can appear after surgery in patients or even in people without surgery. The disease is difficult to diagnose because it is a collection of neurological and mental symptoms. During diagnosis, the doctor usually checks reflexes, muscles and bones, and also orders blood tests and an MRI. Other people may notice the disorder while talking. Sometimes several consultation sessions with specialists are required to confirm the diagnosis.

To date, there is no consensus on the origin and nature of Weber-Cockayne syndrome. With this syndrome, the motor function of the hands suffers; the pathology occurs due to damage to the facial nerve or the pons. At the same time, it was noted that the left side suffers greatly, but the right side is preserved - palmar spasticity occurs on the left side and pronounced asymmetry of the face. Cramps occur first on the left side, and most often begin in the thin muscles of the lower jaw, face, and upper body. Gradually, the cramps develop into muscle spasms on the four limbs and face. At the final stage, seizures cause problems with feeding, swallowing, speaking and orientation.

The clinical picture of VCS syndrome is dominated by such symptoms from the nervous system as monoparesis (arms), focal sensitivity disorders (proprioceptive area of ​​the posterior third of the tongue, quadriplegia, alternating hemiplegia position), hyperkinesia of the facial muscles, hyperkinesia of the tongue, internal ophthalmoplegia. Generalized and combined lower extremity movement disorders are rare, which may indicate the importance of understanding where in the central nervous system the neural elements that regulate the movements of the head, neck, arms and legs are located. Complex dysbasias, accompanied by severe hyperkinetic dysmetria, indicate their localization in the parietal lobe above the thalamic nucleus. Certain manifestations pathognomonic for VCS provide the basis for differentiation from other diseases of the central nervous system and transient brain lesions in various neurological conditions.

The main complaints and symptoms of VKS: impaired statics and coordination of hand movements, cold fingers, trembling; low arm strength, upper limb weakness; convulsive seizure of the hand; Speech is often impaired. The face is amicable, the mouth is half-open, the tongue does not protrude. Asymmetry of the smoothed nasolabial triangle compared with complete asymmetry of the palpebral fissures; when the patient tries to raise an eyebrow, the facial muscles contract; the gaze floats; chokes on his rough, crumbling tongue. Patsi