Fabry Angiokeratoma

Fabry Angiokeratomas are single or multiple disseminated skin lesions of an angular or round shape ranging in size from several millimeters to several centimeters, consisting of numerous closely associated telangiectasias with growths of a hard consistency of a brownish-red color. Clinical signs are most distinct in the first months and years of the disease after telangiectasias, containing cartilage and pigment, are overflowing with red blood cells and typical and typically located arteriosclerotic papules appear on the leg, foot, shoulder and forearm. In the subepidermal papillary formations of peripheral angioxangiosceleros, they form capillaries and essentially turn into thin walls of small and large veins. The size of the skin lesion decreases as the tendency of capillaries to thrombosis increases. Gray and purple telangiosclera gradually disappear, instead of them microscopic plugs with

Fadbry Angiokeratome is a rare hereditary disease that is characterized by the formation of angiomatous nodules in various parts of the body. The name comes from a combination of the Latin word "angio" - vein and the Greek word "kerato" - skin. Fabry angiokeratosis is a serious, extremely rare skin disease in which lesions appear most often in the back and chest and are characterized by small nodular angiopathy of the skin.