Lipoidosis Dystopic Hereditary

Lipoidosis is a non-systemic disease characterized by the formation of fatty plaques in various tissues, especially the liver, central nervous system, pancreas and other organs. One of the main types of lipoids is hereditary dystopic lipoidosis (Dystopic lipidoses), which can

Lipidosis or lipodystrophy is the general name for a group of genetic diseases manifested by the uncontrolled and chronic formation of excess lipids (fats) in the tissues of the body. All diseases of this group are characterized by a benign course without a tendency to metastasize, that is, to spread throughout the body, and are predominantly of hereditary origin or appear from the moment of birth. Even when there are no obvious signs and symptoms, damage to fat cells worsens over time.

Lipodystrophies are divided into forms that differ in the location of excess fat and its sources. There are different types of this disease. Depending on the location and prevalence, the following are distinguished:

Abdominal type If excess lipids are localized only in the fat cells of internal organs (subcutaneous fat and others), the disease is called the abdominal type. Suprarenal form. This is one of the most severe types of dystrophy. Excess fat occurs in the adrenal glands, in the brain and other structures of the body and is life-threatening. The subrenal form of lipodystrophy is caused by excess fat in peripheral organs and parts of the body. This form is most often detected in children. A less common but more dangerous condition is the abdominal form of hyperlipidemia. Fabrial type (lipid cutaneous form) The patient suffers from excessive accumulation of lipid structures in various mucous membranes of the body, on the skin and even in the cornea. This variety is also called lipid-defeating