Naegeli Syndrome

Nägeli syndrome is a type of incontinentia pigmenti. With this disease, in the second year of life, the patient develops pigment spots in the form of a network, which are combined with symmetrical keratoderma. Inheritance occurs along an autosomal dominant line.

In addition, Negel syndrome is a hereditary disease from the group of hemorrhagic diathesis. It is caused by a violation of platelet aglutination processes, which leads to a sharp increase in bleeding time and clot retraction time. Inheritance also occurs according to an autosomal dominant pattern.

Thus, Negeli syndrome is a series of diseases associated with impaired skin pigmentation and impaired platelet aglutination.