Fructosuria, Levulosuria

Fructosuria, Levulosuria is a condition characterized by the presence of fructose (levulose) in the urine.

Fructose and levulose are simple sugars that are normally completely absorbed in the intestines and should not be present in the urine.

The cause of fructosuria and levulesuria is a deficiency of the enzyme aldolase B in the intestine. This enzyme is responsible for the breakdown of fructose and levulose. With its deficiency, these sugars are not absorbed and are excreted in the urine.

Fructosuria and levulesuria are inherited as autosomal recessive diseases. This means that for the disease to manifest, a child must inherit the defective gene from both parents.

These conditions are asymptomatic, since non-absorption of fructose and levulose does not lead to any disorders in the body. Fructosuria and levulesuria are diagnosed only by laboratory testing of urine.

Treatment for fructosuria and levulesuria is not required. It is only recommended to limit foods high in fructose and levulose in the diet to reduce their concentration in urine. The prognosis for these conditions is favorable.

Little fructose is produced in the body due to a deficiency of the enzyme aldolase. However, provided that the enzyme content is less than normal, a large amount of fructosuria is released into the blood. Normally, only fructose passes from the cells of our body into the urine; the longer chain of glucose molecules remains without

Fructosuria (from the Latin fructus - fruit) is a rare hereditary disorder of carbohydrate metabolism with excretion (excretion in the urine) of fruit xyluloses and xyloses. May occur in different forms. The disease got its name because it was first described in children of an African tribe who received citrus fruits containing fruit sugar.