Lortat-Jacob Atrophic Mucosynechial Bullous Dermatitis (E. Lortat-Jacob)

Lorta-Jacob's atrophying mucosinal bullous dermatitis. Lorta Jacob has an ICD code, I can't write it because it belongs to a dermatologist. Epidermolysis bullosa, bullous pemphigoid, familial benign pemphigus of the oral cavity and larynx. Generalized or local bullous dermatitis herpetiformis, bullous dystrophy of the oral cavity. Atrophic cutaneous dystrophy, bullous pemphigiform skin disease (mucosial bullous defect). Lockout

Lorat-Jacques atrophic bullous mucositis of the skin bullous dermatitis (E. Lorat-Jarobi) is a rare skin disease characterized by the formation of inflammatory blisters and mucositis with the formation of ulcers on the skin in the mucous membranes of the mouth, nose, vulva and anus. The disease is named after the French doctor Lorte-Jacou, who gave a detailed description of this pathology. In addition, Lohr-Jacoby syndrome is also distinguished, the peculiarity of which is damage to the central nervous system, liver and lymph nodes.

Lorata-Jacobu pemphigus is characteristic of old age (35-60 years), more common in women. At the onset of the disease, patients note pain when swallowing, talking, and pain around the mouth. White or transparent blisters appear on the mucous membrane of the mouth and cheeks, which merge with each other and form crusts. The exposed surfaces of the tongue are covered with a white, rough coating. Skin lesions are accompanied by itching, burning, and pain. The itching gradually goes away, wounds and ulcers heal. Along with this, various manifestations of inflammation of the mucous membrane of the upper respiratory tract are possible, in some cases the central nervous system is affected.

The course of the disease is rapid, and symptoms begin 2-4 weeks after infection with the varicella zoster virus. Lorta Jacobo is defined by lymphadenopathy six weeks before the appearance of skin lesions. Mostly the rashes are localized on the face and nasopharynx, but the chest, back, and abdomen are also affected. In almost all patients, the disease develops in the gastrointestinal tract.

Usually this disease is unilateral and lasts for several weeks, after which the disease temporarily resolves. The resulting burns are almost always complicated by infection. If left untreated, about 96% of patients die within two years. Diagnosis is made based on a history and examination, and the results of a skin test for autoantibodies. Treatment combines the use of antibacterial drugs and glutamine replacement therapy.

Lortat-Jacob dermatosis is a bullous autoimmune skin reaction. This is a form of pemphigus. Despite the appearance and location, the disease has similar symptoms to other types, such as Hailey-Hailey or Pemphigus congenital benign form, for example. Many features of the disease are also characteristic of other skin diseases. For example, scaly lichen.

The name Lothar Jacques (Lorat-Jacobe) received from a woman who suffered from this disease. Not only was her skin affected, but her cornea was also ulcerated. In 1925, after an autopsy of the victim's body, the cause of the disease was revealed.

Lortat Jacob Atrophic Mucosynachyal Bullous Dermatitis (Lortat Jacob (E Lortet Jacob, 1848-1936)) is a very rare dermatosis. It is a chronic, progressive skin disease characterized by erythema, desquamation, focal erosions and blistering. It is assumed that there is a genetic predisposition to the disease. Prevalence according to the literature is 0.064–0.1 cases per 1 million population. Men get sick more often than women in a ratio of 3.5:1. Behind