Sclerosis Reticularis

Reticular sclerosis (ss) is a rare hereditary disease characterized by dystrophic changes in the vitreous and vascular tracts, retina and peripheral nerve fibers. The disease is most often observed in children and young people and leads to the development of various forms of decreased visual acuity, up to complete blindness.

History of the disease Retinal sclerosis was described in 1928 in two species of monkeys and later discovered in humans. The first clinically significant cases of reticular sclerosis in humans were noted in the 50-60s of the last century. Despite the fact that the causes of the development of the disease have not yet been established, it is one of the types of neurofibromatosis type 1. According to specialized websites, there are more than 300 cases of this disease in people of different age groups. According to the World Health Organization, the overall risk of the disease among the European population is about 1: 175 024, among Africans - 1: 459 602, and among Asians - 1: 518 092. There are two forms of retinal dystrophy: retinal and subretinal, which is characterized by early development of blindness. In addition, it is customary to distinguish primary dystrophy of SET as an independent type of disease. They have unique clinical signs and have different

Reticular sclerosis is a disease characterized by the development of foci of compaction, fibrosis and scarring in the connective tissue of the eye. This chronic inflammatory disease causes irreversible changes in the retina of the eye, which can lead to complete loss of vision.

Typically, retinal sclerosis develops after progressive diseases such as diabetes, hypertension or atherosclerosis. It may also be associated with structural abnormalities of blood vessels