Gerstmann S Syndrome

Gerstmann's Syndrome: Body schema recognition disorder

Introduction

Gerstmann syndrome, also known as Gerstmann-Straussler syndrome, is a rare neurological disorder characterized by partial disintegration of recognition of one's own body schema. This syndrome is named after the German neurologist Joseph Gerstmann, who first described it in 1924. The appearance of symptoms is associated with damage to the associative area of ​​the left parietal lobe of the brain. In this article we will look at the main symptoms and consequences of Gerstmann syndrome.

Main symptoms

Gerstmann syndrome is characterized by a set of symptoms that appear in patients:

  1. Finger Agnosia: Patients have difficulty listing and identifying their own fingers. They may have difficulty indicating which finger is on the left or right and have trouble identifying them.

  2. Side Agnosia: Patients with Gerstmann syndrome are unable to correctly recognize the left and right sides of their own body. They may have difficulty determining whether they are currently to the right or left of other objects or people.

  3. Agraphia: Patients with Gerstmann's syndrome



Hertzmann syndrome, also known as Gerstmann S Syndrome (GS), is a disorder of body recognition with a distorted sense of the right and left sides. The syndrome affects several aspects of body awareness simultaneously, including finger naming, recognition of the right and left sides of the body, and writing and mathematical calculation abilities.

Hertzmann syndrome was originally described in 1975 by James R. Hertzman, an American neurologist who conducted research on parietal lobule lesions. According to him, the disease syndrome was caused by severe disruption of the association areas of the cerebral cortex, which are associated with the functions of processing space and direction



Hermann-Pudlak syndrome is a genetic disease of the peripheral nervous system; it is characterized by progressive muscle weakness and atrophy, endocrine disorders, and decreased sensitivity. Often the patient loses his ability to work at the age of 30–40.

Disease history

The first description of Hermann-Pudlak syndrome was published in 1978. Two brothers suffered from this disease: 45-year-old industrial engineer Erich Germanz and his son 20-year-old Alexander Germanz. The syndrome was confirmed by neuropathologist Detlef Lederbusch, who noticed an unusual gait - the patient was unsteady